Erythromelanosis follicularis faciei et colli (EFF)

[Guide]

Abstract
Erythromelanosis follicularis faciei et colli (EFF) is an unusual condition characterized by the triad of hyperpigmentation, follicular plugging and erythema of face and neck. This is less common in women and familial case reports are few. We report EFF in three siblings in an Indian family, two of whom are females. The possibility of this condition being genetically related to keratosis pilaris as well as being a variant of keratosis rubra pilaris is also discussed.

IDJVL 2008  |  Volume : 74  |  Issue : 1  |  Page : 47-49
Erythromelanosis follicularis faciei et colli: Relationship with keratosis pilaris
M Augustine, E Jayaseelan
Department of Dermatology, St. John's Medical College Hospital, Bangalore, India

----------------------

Abstract
The thirteenth case of erythromelanosis follicularis of the face and neck is reported and attention is called to this entity. Characteristically, it affects males in adolescence or young adulthood. It begins symmetrically on the preauricular cheeks and imperceptibly spreads onto the temples and lateral aspects of the neck. It presents as an irregularly marginated, red-brown pigmentation with fine telangiectasia, small, pale, slightly scaly, follicular papules, and patchy alopecia of vellus hair. The histologic features, although nondiagnostic, correlate well with the clinical features. The possible relationship to keratosis pilaris rouge is discussed.

JAAD, November 1981 Volume 5, Issue 5, Pages 533–534
Erythromelanosis follicularis faciei et colli
A case report
Thomas L. Watt, M.D., John S. Kaiser, M.D.
Bangor, ME, USA
From the Departments of Medicine (Section of Dermatology) and Pathology of the Eastern Maine Medical Center.

---------------------------------------------------------------------------------------------------------------------

"In view of its association with keratosis pilaris at arms and shoulders, this condition may be more common than previously thought but prevalence studies are lacking. Rosacea is a chronic facial dermatosis characterized by central facial erythema and flushing with varying presentations comprising papules, pustules, phymatous features and ocular irritation. Childhood and adolescent rosacea has been noted in case reports and case series."

Indian Journal of Dermatology, Venereology and Leprology 74(1):47-January 2008
Erythromelanosis follicularis faciei et colli: Relationship with keratosis pilaris

--------------------------------------

Images